Extreme oral manifestations in a Marfan-type syndrome

(a) Reduced elbow extension <170°, true dolichostenomelia; (b) lateral facial views; (c) lateral Delaire's cephalometry showing skeletal class I, vertical anterior excess and open mandibular angle.

(a) Frontal bite views showing numerous dental mispositions; (b) orthopantomogram showing supernumerary teeth, pachydontia and dental crowding; (c) 3D reconstructions of jaw CT scan; extreme dental crowding and numerous included teeth.

(a) Right maxillary molar (section) showing abnormal crown and pulpoliths; (b) thin mineralized slice of dental tissue (supernumerary molar) under polarized microscopy showing typical concentric architecture of pulpoliths at the limit between dentin and pulp next to zones with disorganized dentin (scale bar: 1mm); (c) same preparation showing a single pulpolith in the pulpar cavity with radiating canaliculi (scale bar: 200μm).